PEX14 acts as the interface linking optineurin to cell type-selective pexophagy DOI Open Access
Hongli Li, Suyuan Chen, Celien Lismont

и другие.

bioRxiv (Cold Spring Harbor Laboratory), Год журнала: 2024, Номер unknown

Опубликована: Май 31, 2024

Abstract Pexophagy, the selective degradation of peroxisomes, is essential for removing excess or dysfunctional and its dysregulation linked to various diseases. Previous research has shown that optineurin (OPTN), an autophagy receptor involved in mitophagy, aggrephagy, xenophagy, can induce pexophagy HEK-293 cells. However, underlying mechanism remains unclear. In this study, we used proximity labeling identify PEX14, a peroxisomal membrane protein, as neighboring partner OPTN. Biochemical analyses revealed PEX14 OPTN interact through their respective coiled-coil ubiquitin-binding domains. Further demonstrated C-terminal half overexpressed triggers pexophagy, likely by forming oligomers with endogenous The co-localization PEX14-OPTN complexes LC3, combined suppression OPTN-mediated peroxisome bafilomycin A1, supports model which acts docking site on membrane, enabling recruitment autophagic machinery pexophagy. Summary This study uncovers defines protein key player optineurin-driven advancing our mechanistic understanding cellular process. These findings open new avenues developing therapeutic strategies targeting diseases associated defective

Язык: Английский

Peroxisomal ether-glycerophospholipid synthesis is dysregulated after TBI. DOI Creative Commons

Amir Mehrabani-Tabari,

Nivedita Hegdekar,

Sabrina Bustos

и другие.

Journal of Lipid Research, Год журнала: 2025, Номер unknown, С. 100821 - 100821

Опубликована: Май 1, 2025

Ether-glycerophospholipids (ether-GPs), the ether bond- (- O -) containing glycerophospholipids are major components of brain lipidome. Ether-GPs play a crucial role in regulating neuronal function, and their deficiency has been implicated many neurodegenerative diseases. However, how they affected after traumatic injury (TBI) is not known. Our data demonstrate significant decrease ether-GPs abundance mouse cortex following controlled cortical impact (CCI) induced TBI. This at least part due to impairment peroxisomal ether-GP synthesis We detected dysregulation synthesizing enzymes - glyceronephosphate-O-acyltransferase (GNPAT) alkylglycerone phosphate synthase (AGPS) injured brains. decline GNPAT level fraction marked accumulation AGPS cytosol cortices To restore brain, we treated TBI mice with an precursor 1-O-octadecylglycerol (OAG) bypass steps. OAG partially restored levels several ether-GPs, attenuated inflammatory cytokine expression improved functional recovery Taken together, our that restoration by treatment can improve outcomes.

Язык: Английский

Процитировано

0

Dysregulation of autophagy during photoaging reduce oxidative stress and inflammatory damage caused by UV DOI Creative Commons

Zhongsong Zhang,

Ru Yu Tan, Zhengang Xiong

и другие.

Frontiers in Pharmacology, Год журнала: 2025, Номер 16

Опубликована: Май 12, 2025

Photoaging, the premature aging of skin due to chronic ultraviolet (UV) exposure, is a growing concern in dermatology and cosmetic science. While UV radiation known induce DNA damage, oxidative stress, inflammation cells, recent research unveils promising countermeasure: autophagy. This review explores intricate relationship between autophagy photoaging, highlighting how this cellular recycling process can mitigate UV-induced damage. We begin by examining differential impacts UVA UVB on cells role stress accelerating photoaging. Next, we delve into molecular mechanisms autophagy, including its various forms regulatory pathways. Central discussion autophagy's protective functions, such as clearance damaged organelles proteins, maintaining genomic integrity. Furthermore, address current challenges harnessing for therapeutic purposes, need selective inducers deeper understanding context-dependent effects. By synthesizing advancements proposing future directions, underscores potential modulation novel strategy prevent treat comprehensive analysis aims inspire further investigation autophagy-based interventions, offering new hope preserving health face environmental stressors.

Язык: Английский

Процитировано

0

Revisiting the Pathogenesis of X-Linked Adrenoleukodystrophy DOI Open Access
Pierre Bougnères, Catherine Le Stunff

Genes, Год журнала: 2025, Номер 16(5), С. 590 - 590

Опубликована: Май 17, 2025

Background: X-ALD is a white matter (WM) disease caused by mutations in the ABCD1 gene encoding transporter of very-long-chain fatty acids (VLCFAs) into peroxisomes. Strikingly, same mutation causes either devastating brain inflammatory demyelination during childhood or, more often, progressive spinal cord axonopathy starting middle-aged adults. The accumulation undegraded VLCFA glial cell membranes and myelin has long been thought to be central mechanism X-ALD. Methods: This review discusses studies mouse drosophila models that have modified our views pathogenesis. Results: In Abcd1 knockout (KO) mimics disease, late manifestations are rapidly reversed transfer oligodendrocytes (OLs). peroxin-5 KO model, selective impairment peroxisomal biogenesis OLs achieves an almost perfect phenocopy cerebral ALD. A model revealed myelinating cells production toxic lipid able poison axons activate cells. Other showed critical role providing energy substrates axons. addition, on microglial changing substates improved understanding neuroinflammation. Conclusions: Animal supporting primary axonal pathology secondary microglia allow us revisit mechanisms. Beyond mutations, pathogenesis depends unidentified contributors, such as genetic background, cell-specific epigenomics, potential environmental triggers, stochasticity crosstalk between multiple types among billions neurons.

Язык: Английский

Процитировано

0

PEX14 acts as the interface linking optineurin to cell type-selective pexophagy DOI Open Access
Hongli Li, Suyuan Chen, Celien Lismont

и другие.

bioRxiv (Cold Spring Harbor Laboratory), Год журнала: 2024, Номер unknown

Опубликована: Май 31, 2024

Abstract Pexophagy, the selective degradation of peroxisomes, is essential for removing excess or dysfunctional and its dysregulation linked to various diseases. Previous research has shown that optineurin (OPTN), an autophagy receptor involved in mitophagy, aggrephagy, xenophagy, can induce pexophagy HEK-293 cells. However, underlying mechanism remains unclear. In this study, we used proximity labeling identify PEX14, a peroxisomal membrane protein, as neighboring partner OPTN. Biochemical analyses revealed PEX14 OPTN interact through their respective coiled-coil ubiquitin-binding domains. Further demonstrated C-terminal half overexpressed triggers pexophagy, likely by forming oligomers with endogenous The co-localization PEX14-OPTN complexes LC3, combined suppression OPTN-mediated peroxisome bafilomycin A1, supports model which acts docking site on membrane, enabling recruitment autophagic machinery pexophagy. Summary This study uncovers defines protein key player optineurin-driven advancing our mechanistic understanding cellular process. These findings open new avenues developing therapeutic strategies targeting diseases associated defective

Язык: Английский

Процитировано

0