Elucidating the Impact of Deleterious Mutations on IGHG1 and Their Association with Huntington’s Disease DOI Open Access
Alaa Shafie, Amal Adnan Ashour, Farah Anjum

и другие.

Journal of Personalized Medicine, Год журнала: 2024, Номер 14(4), С. 380 - 380

Опубликована: Апрель 1, 2024

Huntington's disease (HD) is a chronic, inherited neurodegenerative condition marked by chorea, dementia, and changes in personality. The primary cause of HD mutation characterized the expansion triplet repeat (CAG) within huntingtin gene located on chromosome 4. Despite substantial progress elucidating molecular cellular mechanisms HD, an effective treatment for this disorder not available so far. In recent years, researchers have been interested studying cerebrospinal fluid (CSF) as source biomarkers that could aid diagnosis therapeutic development disorder. Immunoglobulin heavy constant gamma 1 (IGHG1) one CSF proteins found to increase significantly HD. Considering this, it reasonable study potential involvement deleterious mutations IGHG1 pathogenesis study, we explored impact their subsequent association with We evaluated 126 single-point amino acid substitutions structure functionality protein while exploiting multiple computational resources such SIFT, PolyPhen-2, FATHMM, SNPs&Go mCSM, DynaMut2, MAESTROweb, PremPS, MutPred2, PhD-SNP. sequence- structure-based tools highlighted 10 were destabilizing. Subsequently, out these mutations, eight variants (Y32C, Y32D, P34S, V39E, C83R, C83Y, V85M, H87Q) identified pathogenic phenotype predictors. Finally, two (Y32C P34S) reduce solubility protein, suggesting propensity form aggregates. These also exhibited higher residual frustration structure. findings, hypothesized may compromise its function potentially contribute pathogenesis.

Язык: Английский

Seven Hub Genes Associated with Huntington’s Disease and Diagnostic and Therapeutic Potentials Identified by Computational Biology DOI
Afzal Hussain, Taj Mohammad, Shumayila Khan

и другие.

OMICS A Journal of Integrative Biology, Год журнала: 2025, Номер unknown

Опубликована: Март 10, 2025

Huntington's disease (HD) is characterized by progressive motor dysfunction and cognitive decline. Early diagnosis new therapeutic targets are essential for effective interventions. We performed integrative analyses of mRNA profiles from three microarrays one RNA-seq dataset the Gene Expression Omnibus database. The datasets included were GSE8762, GSE24250, GSE45516, GSE64810. Data pre-processing background correction, normalization, log2 transformation, probe-to-gene symbol mapping, differential expression analysis. identified 80 differentially expressed genes (DEGs) based on a significance threshold (p < 0.05) absolute log fold change (logFC) >0.65. Additionally, we conducted Ontology (GO) pathway genes. Protein-protein interactions among DEGs revealed network which seven hub (VIM, COL1A1, COL3A1, COL1A2, DCN, CXCR2, S100A9) using cytoHubba plugin in Cytoscape software. Two top DEGs, IGHG1 (up-regulated) PITX1 (up-regulated), also hold potential as targets. Insofar biological contextualization findings concerned, enriched GO terms skeletal system development, blood vessel vasculature development. Molecular function highlighted signaling receptor binding, extracellular matrix structural constituent, platelet-derived growth factor binding. Notably, significant KEGG pathways amoebiasis, AGE-RAGE diabetic complications, relaxin pathway. In conclusion, present computational biology multiple discovered genes, shedding light molecular mechanisms HD. These call translational clinical omics research may potentially lead to future precision medicine interventions novel diagnostic biomarkers

Язык: Английский

Процитировано

0

Elucidating the Impact of Deleterious Mutations on IGHG1 and Their Association with Huntington’s Disease DOI Open Access
Alaa Shafie, Amal Adnan Ashour, Farah Anjum

и другие.

Journal of Personalized Medicine, Год журнала: 2024, Номер 14(4), С. 380 - 380

Опубликована: Апрель 1, 2024

Huntington's disease (HD) is a chronic, inherited neurodegenerative condition marked by chorea, dementia, and changes in personality. The primary cause of HD mutation characterized the expansion triplet repeat (CAG) within huntingtin gene located on chromosome 4. Despite substantial progress elucidating molecular cellular mechanisms HD, an effective treatment for this disorder not available so far. In recent years, researchers have been interested studying cerebrospinal fluid (CSF) as source biomarkers that could aid diagnosis therapeutic development disorder. Immunoglobulin heavy constant gamma 1 (IGHG1) one CSF proteins found to increase significantly HD. Considering this, it reasonable study potential involvement deleterious mutations IGHG1 pathogenesis study, we explored impact their subsequent association with We evaluated 126 single-point amino acid substitutions structure functionality protein while exploiting multiple computational resources such SIFT, PolyPhen-2, FATHMM, SNPs&Go mCSM, DynaMut2, MAESTROweb, PremPS, MutPred2, PhD-SNP. sequence- structure-based tools highlighted 10 were destabilizing. Subsequently, out these mutations, eight variants (Y32C, Y32D, P34S, V39E, C83R, C83Y, V85M, H87Q) identified pathogenic phenotype predictors. Finally, two (Y32C P34S) reduce solubility protein, suggesting propensity form aggregates. These also exhibited higher residual frustration structure. findings, hypothesized may compromise its function potentially contribute pathogenesis.

Язык: Английский

Процитировано

3