Evaluation of cyanotoxin L-BMAA effect on α-synuclein and TDP43 proteinopathy DOI Creative Commons
Paola Sini, Grazia Galleri, Cristina Ciampelli

et al.

Frontiers in Immunology, Journal Year: 2024, Volume and Issue: 15

Published: March 26, 2024

The complex interplay between genetic and environmental factors is considered the cause of neurodegenerative diseases including Parkinson’s disease (PD) Amyotrophic Lateral Sclerosis (ALS). Among factors, toxins produced by cyanobacteria have received much attention due to significant increase in growth worldwide. In particular, L-BMAA toxin, diverse taxa cyanobacteria, dinoflagellates diatoms, has been extensively correlated neurodegeneration. molecular mechanism neurotoxicity still cryptic far from being understood. this research article, we investigated pathways altered exposure cell systems, highlighting a specific stress an impairment autophagic processes. Interestingly, these changes lead accumulation both α-synuclein TDP43, which are with PD ALS proteinopathy, respectively. Finally, were able demonstrate alterations TDP43 WT or pathological mutants respect protein accumulation, aggregation cytoplasmic translocation, some typical features sporadic familial ALS.

Language: Английский

Aging-Associated Amyloid-β Plaques and Neuroinflammation in Bottlenose Dolphins (Tursiops truncatus) and Novel Cognitive Health-Supporting Roles of Pentadecanoic Acid (C15:0) DOI Open Access
Stephanie Venn‐Watson, Eric D. Jensen

International Journal of Molecular Sciences, Journal Year: 2025, Volume and Issue: 26(8), P. 3746 - 3746

Published: April 16, 2025

There is an urgent need to identify interventions that broadly target aging-related cognitive decline and progression Alzheimer’s disease (AD). Bottlenose dolphins (Tursiops truncatus) have histologic changes similar AD in humans, they also develop shared age-associated co-morbidities identified as risk factors for including type 2 diabetes, ferroptosis, iron overload, which can be driven by nutritional C15:0 deficiency. We hypothesized (1) would amyloid beta (Aβ) plaques neuroinflammation paralleled of humans relation age-related progression, quantitative concentration, brain region; (2) dose-dependent activities relevant protecting health. Quantitative immunohistochemistry staining was used assess 68 tissues from archived brains 19 Navy evaluate associations among region, sex, age group. Further, activities, using a third-party panel intended screen potential therapeutics, were evaluated. Similar had the highest Aβ plaque density variation hippocampus (90th percentile 4.95 plaques/mm2), where increased with (p = 0.05). All measured markers detected, concentrations activated microglia (CD68+) (0.46 ± 0.38 cells/mm2). inhibitor two targets, fatty acid amide hydrolase (FAAH) (IC50 2.5 µM, 89% maximum inhibition at 50 µM relative URB597) monoamine oxidase B (MAO-B) 19.4 70% R(-)-Deprenyl). These demonstrated efficacy against formation neuroinflammation, protection function hippocampus. findings suggest that, addition co-morbidities, may play distinct role supporting health, especially higher concentrations.

Language: Английский

Citations

0

Alzheimer’s Disease Neuropathological Change in Aged Non-Primate Mammals DOI Open Access
Isidró Ferrer

International Journal of Molecular Sciences, Journal Year: 2024, Volume and Issue: 25(15), P. 8118 - 8118

Published: July 25, 2024

Human brain aging is characterized by the production and deposition of β-amyloid (Aβ) in form senile plaques cerebral amyloid angiopathy intracellular accumulation hyper-phosphorylated tau (Hp-tau) to neurofibrillary tangles (NFTs) dystrophic neurites plaques. The process progresses for years eventually manifests as cognitive impairment dementia a subgroup aged individuals. Aβ produced deposited first neocortex most mammals, including humans; it usually not accompanied altered behavior impairment. Hp-tau less frequent than pathology, NFTs are rare mammals. In contrast, familiar from middle age onward appear paleocortex selected stem nuclei. precede decades or correlate with about 5% individuals at 65 25% 85. Based on these comparative data, (a) common Alzheimer’s disease neuropathological change (ADNC) mammals; (b) common, however, principal cytoskeletal pathology (c) NFT humans starts nuclei paleocortical regions progressing parts other telencephalon; (d) human unique among mammalian species due early appearance dramatic progression onward, matching advanced cases; (e) neither nor supports concept cascade hypothesis.

Language: Английский

Citations

2

Amyloid-β and phosphorylated tau screening in bottlenose dolphin (Tursiops truncatus) and striped dolphin (Stenella coeruleoalba) brains from Italy reveals distinct immunohistochemical patterns correlating with age and co-morbidity DOI Creative Commons
Ksenia Orekhova, Camilla Testori, Federica Giorda

et al.

PLoS ONE, Journal Year: 2024, Volume and Issue: 19(11), P. e0314085 - e0314085

Published: Nov. 26, 2024

Cetacean brains are uniquely adapted to diving, but can be affected by diseases and exposure toxins, triggering neurodegenerative processes that may cause stranding. Some species exhibit a significant post-reproductive lifespan (PRLS), increasing the likelihood of observing cumulative age-related pathology. Immunohistochemistry against amyloid-β hyperphosphorylated tau proteins is increasingly implemented assess Alzheimer’s Disease-like neuropathology in cetaceans, comparisons between geographically distinct populations, animals different age groups, sex, with concomitant pathologies lacking. We tested 43 cetaceans’ (30 Tursiops truncatus ; 13 Stenella coeruleoalba ) parietal cortex, our most consistently archived cerebral tissue, immunohistochemical analyses oligomer 42 (Aβ-42) (pTau AT180 AT8) antibodies. Aβ-42 antibody cross-reacted plaques three aged bottlenose two striped dolphins, was more often detected within neurons, glia, blood vessels all dolphins. Histoscore dolphins ages, sexes, revealed correlations older age, viral infections, plaque presence. Protozoan cysts antibody. pTau signal observed as single foci neurons neuropil young To knowledge, this study first its kind for Mediterranean region will help establish baseline understanding physiological pathological expression associated human disease cetacean brains.

Language: Английский

Citations

1

Mechanisms of intestinal injury in polychaete Perinereis aibuhitensis caused by low-concentration fluorene pollution: Microbiome and metabonomic analyses DOI
Teng Teng, Yuting Yang, Huihong Li

et al.

Journal of Hazardous Materials, Journal Year: 2024, Volume and Issue: 475, P. 134925 - 134925

Published: June 15, 2024

Language: Английский

Citations

0

Editorial: New insights in the neuroanatomy and neuropathology of marine mammals DOI Creative Commons
Simona Sacchini, Cristiano Bombardi

Frontiers in Neuroanatomy, Journal Year: 2024, Volume and Issue: 18

Published: July 1, 2024

Keywords: neuroanatomy, neuropathology, neurodegenerative diseases, marine mammals, cetaceans, toothed whales, planetary health

Language: Английский

Citations

0

Central Nervous System Disorders of Marine Mammals: Models for Human Disease? DOI Creative Commons
Giovanni Di Guardo

Pathogens, Journal Year: 2024, Volume and Issue: 13(8), P. 684 - 684

Published: Aug. 14, 2024

This article deals with Central Nervous System (CNS) disorders of marine mammals as putative neuropathology and neuropathogenesis models for their human and, to some extent, animal “counterparts” in a dual “One Health” “Translational Medicine” perspective. Within this challenging context, special emphasis is placed upon Alzheimer’s disease (AD), provided that AD-like pathological changes have been reported the brain tissue stranded cetacean specimens belonging different Odontocete species. Further examples potential comparative pathology interest are represented by viral infections particular, “Subacute Sclerosing Panencephalitis” (SSPE), rare neurologic sequela patients infected Measles virus (MeV). Indeed, Cetacean morbillivirus (CeMV)-infected striped dolphins (Stenella coeruleoalba) may also develop “brain-only” form CeMV infection, sharing neuropathological similarities SSPE. framework, global threat A(H5N1) avian influenza another major concern issue, severe meningoencephalitis occurring affected pinnipeds cetaceans, similarly what seen beings. Finally, role Brucella ceti-infected, neurobrucellosis-affected cetaceans counterparts analyzed discussed. Notwithstanding above, much more work needed before drawing conclusion mammal CNS mirror “analogues”.

Language: Английский

Citations

0

Perivascular phosphorylated TDP‐43 inclusions are associated with Alzheimer's disease pathology and loss of CD146 and Aquaporin‐4 DOI Creative Commons
J. Rubio Santiago,

Dovilė Pocevičiūtė,

Malin Wennström

et al.

Brain Pathology, Journal Year: 2024, Volume and Issue: unknown

Published: Sept. 9, 2024

Abstract The majority of patients with Alzheimer's disease (AD) exhibit aggregates Trans‐active response DNA binding protein 43 (TDP‐43) in their hippocampus, which is associated a more aggressive progression. TDP‐43 inclusions are commonly found neurons, but also astrocytes. impact the astrocytes less known. In current study, we investigate presence phosphorylated (pTDP‐43) astrocytic endfeet and potential association blood–brain barrier (BBB) damage, glymphatic system dysfunction, AD pathology. By staining postmortem hippocampal sections from non‐demented controls against pTDP‐43 together markers glial fibrillary acidic (GFAP), marker Aquaporin‐4 (AQP4), for BBB alterations (CD146) leakiness (Immunoglobulin A), demonstrate close between perivascular or GFAP AQP4. These were prominent correlated severity loss CD146 findings indicate relationship accumulation may contribute to downstream pathological events seen

Language: Английский

Citations

0

Neurodegenerative Diseases: What Can Be Learned from Toothed Whales? DOI Creative Commons
Simona Sacchini

Neuroscience Bulletin, Journal Year: 2024, Volume and Issue: unknown

Published: Nov. 1, 2024

Neurodegeneration involves a wide range of neuropathological alterations affecting the integrity, physiology, and architecture neural cells. Many studies have demonstrated neurodegeneration in different animals. In case Alzheimer's disease (AD), spontaneous animal models should display two neurohistopathological hallmarks: deposition β-amyloid arrangement neurofibrillary tangles. However, no natural that fulfill these conditions been reported most research into AD has performed using transgenic rodents. Recent also toothed whales - homeothermic, long-lived, top predatory marine mammals show signs AD-like pathology. The hallmarks cetaceans could help to better understand their endangered health as well neurodegenerative diseases humans. This systematic review analyzes all literature published date on this trending topic proposed causes for iconic are approached context One Health/Planetary Health translational medicine.

Language: Английский

Citations

0

Evaluation of cyanotoxin L-BMAA effect on α-synuclein and TDP43 proteinopathy DOI Creative Commons
Paola Sini, Grazia Galleri, Cristina Ciampelli

et al.

Frontiers in Immunology, Journal Year: 2024, Volume and Issue: 15

Published: March 26, 2024

The complex interplay between genetic and environmental factors is considered the cause of neurodegenerative diseases including Parkinson’s disease (PD) Amyotrophic Lateral Sclerosis (ALS). Among factors, toxins produced by cyanobacteria have received much attention due to significant increase in growth worldwide. In particular, L-BMAA toxin, diverse taxa cyanobacteria, dinoflagellates diatoms, has been extensively correlated neurodegeneration. molecular mechanism neurotoxicity still cryptic far from being understood. this research article, we investigated pathways altered exposure cell systems, highlighting a specific stress an impairment autophagic processes. Interestingly, these changes lead accumulation both α-synuclein TDP43, which are with PD ALS proteinopathy, respectively. Finally, were able demonstrate alterations TDP43 WT or pathological mutants respect protein accumulation, aggregation cytoplasmic translocation, some typical features sporadic familial ALS.

Language: Английский

Citations

0